Pathways of ammonia detoxification to GLN in muscles related to Improved use on the BCAA and ?-KG (cataplerosis) and recommended outcomes of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Optimistic outcome of BCAA on ammonia detoxification to GLN could be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylbutyr